McManaman J, Tam D A
Department of Pediatrics and Clinical Investigations, Naval Medical Center San Diego, California 92134-1005, USA.
Pediatr Neurol. 1999 May;20(5):381-2. doi: 10.1016/s0887-8994(98)00166-0.
Self-injurious behavior is a common clinical problem in children with Lesch-Nyhan syndrome, an X-linked disorder of purine metabolism. This behavior is not observed in other conditions associated with increased serum concentrations of uric acid, hypoxanthine, and xanthine. Various neurotransmitters appear to play a pivotal role in self-injurious behavior. The authors present a patient with Lesch-Nyhan syndrome, whose self-injurious behavior was effectively treated with gabapentin, and discuss possible mechanisms of action.
自伤行为是莱施-奈恩综合征患儿中常见的临床问题,莱施-奈恩综合征是一种嘌呤代谢的X连锁疾病。在与血清尿酸、次黄嘌呤和黄嘌呤浓度升高相关的其他病症中未观察到这种行为。各种神经递质似乎在自伤行为中起关键作用。作者介绍了一名患有莱施-奈恩综合征的患者,其自伤行为通过加巴喷丁得到有效治疗,并讨论了可能的作用机制。