Ikeda S, Sera Y, Yoshida M, Izaki T, Uchino S, Endo F, Ohmuraya M, Beppu T
Department of Pediatric Surgery, Kumamoto University Medical School, Honjo, Japan.
J Pediatr Surg. 1999 Jun;34(6):1031-2. doi: 10.1016/s0022-3468(99)90785-6.
The authors report the case of a 7-month-old Japanese infant with congenital intrahepatic portosystemic shunts. He had hypergalactosaemia and hyperammonemia at age 1 month. The diagnosis was made by ultrasonography and angiography. Coil embolization was performed successfully, and then hyperammonemia and hypergalactosaemia improved soon after surgery.
作者报告了一例患有先天性肝内门体分流的7个月大日本婴儿的病例。他在1个月大时出现高半乳糖血症和高氨血症。诊断通过超声检查和血管造影做出。成功进行了弹簧圈栓塞术,术后高氨血症和高半乳糖血症很快得到改善。