Department of Radiology, Dankook University College of Medicine, Dankook University Hospital, Chungcheongnam-do, Korea.
Korean J Radiol. 2010 Sep-Oct;11(5):583-6. doi: 10.3348/kjr.2010.11.5.583. Epub 2010 Aug 27.
A congenital intrahepatic portosystemic shunt is a rare anomaly; but, the number of diagnosed cases has increased with advanced imaging tools. Symptomatic portosystemic shunts, especially those that include hyperammonemia, should be treated; and various endovascular treatment methods other than surgery have been reported. Hepatic masses with either an intra- or extrahepatic shunt also have been reported, and the mass is another reason for treatment. Authors report a case of a congenital intrahepatic portosystemic shunt with a hepatic mass that was successfully treated using a percutaneous endovascular approach with vascular plugs. By the time the first short-term follow-up was conducted, the hepatic mass had disappeared.
先天性肝内门体分流是一种罕见的异常;但是,随着先进的成像工具的发展,诊断出的病例数量有所增加。有症状的门体分流,特别是伴有血氨升高的分流,应进行治疗;除手术外,还报道了各种血管内治疗方法。既有肝内分流又有肝外分流的肝肿块也有报道,肿块也是治疗的另一个原因。作者报告了一例先天性肝内门体分流伴肝肿块的病例,该病例通过血管塞的经皮血管内方法成功治疗。在进行第一次短期随访时,肝肿块已经消失。