Roganovich J, Bisogno G, Cecchetto G, D'Amore E S, Carli M
Division of Hematology/Oncology, Department of Pediatrics, University of Padova, Padova, Italy.
J Surg Oncol. 1999 Aug;71(4):269-72. doi: 10.1002/(sici)1096-9098(199908)71:4<269::aid-jso13>3.0.co;2-m.
Desmoplastic small round cell tumor (DSRCT) is a rare neoplasm mainly affecting young males and typically located in the abdomen. Prognosis is generally very poor. We report a rare case of paratesticular DSRCT in a 17-year-old boy, presenting with an isolated left scrotal mass. The patient had an excellent outcome after complete surgical resection of the tumor and adjuvant multi-agent chemotherapy. DSRCT should be included in the differential diagnosis of small round cell tumors of the paratesticular region in adolescents and young adults. Tumor resection and chemotherapy may be beneficial for these patients. Our experience and a review of the literature suggest that DSRCT located in the paratesticular region may have a better prognosis than its more frequent abdominal counterpart.
促结缔组织增生性小圆细胞肿瘤（DSRCT）是一种罕见的肿瘤，主要影响年轻男性，通常位于腹部。预后一般很差。我们报告了一例罕见的17岁男孩睾丸旁DSRCT病例，表现为孤立的左侧阴囊肿块。患者在肿瘤完全手术切除及辅助多药化疗后取得了良好的疗效。DSRCT应纳入青少年和年轻成人睾丸旁区域小圆细胞肿瘤的鉴别诊断。肿瘤切除和化疗可能对这些患者有益。我们的经验及文献回顾表明，位于睾丸旁区域的DSRCT可能比更常见的腹部DSRCT预后更好。
