Erkan F
Division of Pneumology, Istanbul Medical Faculty, University of Istanbul, Capa/Istanbul, Turkey.
Curr Opin Pulm Med. 1999 Sep;5(5):314-8. doi: 10.1097/00063198-199909000-00009.
Pulmonary artery aneurysms varying in size and number continue to be the principal feature of pulmonary involvement in Behçet disease (BD). Pulmonary aneurysms have been reported to be associated with cardiac thromboses, mainly in the right heart. Bronchiolitis obliterans organizing pneumonia has also been seen in the setting of pulmonary artery aneurysms. Aneurysms of the aortic arch and subclavian artery are rarely recognized thoracic manifestations of BD. Noninvasive imaging techniques, such as helical computed tomography and magnetic resonance angiography, are the safer and preferred methods for identifying aneurysms and thrombi. Digital substraction angiography has been found to be inadequate in showing thrombosed vessels. Follow-up computed tomography was performed in the documentation of the aneurysmal healing process. In patients receiving immunosuppressive treatment, intramural thrombus formation occurred and was followed by aneurysmal regression and disappearance. General principles for the treatment of systemic vasculitis are used in the treatment of BD.
大小和数量各异的肺动脉瘤仍然是白塞病（BD）肺部受累的主要特征。据报道，肺动脉瘤与心脏血栓形成有关，主要发生在右心。在肺动脉瘤的情况下也可见闭塞性细支气管炎伴机化性肺炎。主动脉弓和锁骨下动脉的动脉瘤是BD罕见的胸部表现。螺旋计算机断层扫描和磁共振血管造影等非侵入性成像技术是识别动脉瘤和血栓更安全且首选的方法。已发现数字减影血管造影在显示血栓形成的血管方面不足。采用随访计算机断层扫描记录动脉瘤的愈合过程。在接受免疫抑制治疗的患者中，出现了壁内血栓形成，随后动脉瘤消退并消失。BD的治疗采用系统性血管炎的一般治疗原则。
