York A, von Fraunhofer N, Turk J, Sedgwick P
Department of General Psychiatry, Jenner Wing, St George's Hospital Medical School, London, UK.
J Intellect Disabil Res. 1999 Aug;43 ( Pt 4):314-24. doi: 10.1046/j.1365-2788.1999.00219.x.
Fragile-X syndrome is the commonest cause of inherited intellectual disability. There is good evidence for a behavioural phenotype. This has implications for school staff using standard educational techniques. Similarly, autism is known to create particular educational requirements. The present study examined the awareness and knowledge of fragile-X syndrome, Down's syndrome and autism amongst staff in special and mainstream education. One hundred and two special school staff and 40 mainstream school staff completed questionnaires. Most staff offered a variety of features 'typical' of Down's syndrome and autism. In contrast, staff knew less about fragile-X syndrome. Specific knowledge about the learning styles of these children was very poor, but was associated with having taught an affected child. Mainstream and special school staff offered similar levels of knowledge for all three conditions. Staff did not demonstrate a sufficiently specialized knowledge of fragile-X syndrome to ensure that the special educational needs of these children were being met fully.
脆性X综合征是遗传性智力残疾最常见的病因。有充分证据表明其存在行为表型。这对使用标准教育技术的学校工作人员有影响。同样，众所周知自闭症有特定的教育需求。本研究调查了特殊教育和主流教育工作人员对脆性X综合征、唐氏综合征和自闭症的认识和了解。102名特殊学校工作人员和40名主流学校工作人员完成了问卷调查。大多数工作人员列举了唐氏综合征和自闭症的各种“典型”特征。相比之下，工作人员对脆性X综合征了解较少。关于这些孩子学习方式的具体知识非常匮乏，但与曾教过患病孩子有关。主流学校和特殊学校工作人员对这三种情况的了解程度相近。工作人员对脆性X综合征没有表现出足够的专业知识，无法确保这些孩子的特殊教育需求得到充分满足。
