Kabaker M, Casasoprana A, Estampes B, Magnier S, Galey J J, Vernant P
Arch Mal Coeur Vaiss. 1978 Oct;71(10):1160-5.
A child of 10 was admitted to a cardiology unit with adiastole. The marked degree of dwarfism and anatomical features were characteristic of the so-called 'Mulibrey' dwarfism. Surgical intervention confirmed the constrictive pericarditis which is normally found in this condition. Unfortunately, the adiastole persisted which, taking into account the marked eosinophilia, made an associated endomyocardial fibrosis seem likely. The distinctive features of constrictive pericarditis and of the constrictive type of cardiomyopathy are recalled.
一名10岁儿童因舒张期功能障碍入住心脏病科。明显的侏儒症程度和解剖特征是所谓“穆利布雷(Mulibrey)”侏儒症的典型表现。手术干预证实存在缩窄性心包炎,这在该病症中较为常见。不幸的是,舒张期功能障碍持续存在,考虑到明显的嗜酸性粒细胞增多,提示可能合并有心肌内膜纤维化。文中回顾了缩窄性心包炎和缩窄型心肌病的显著特征。