Jirari A, Charpentier A, Popescu S, Boidin P, Eisenmann B
Department of Cardiovascular Surgery, Hospital Civil de Strasbourg, France.
Ann Thorac Surg. 1999 Aug;68(2):565-6. doi: 10.1016/s0003-4975(99)00572-x.
We report the case of a malignant primary cardiac pheochromocytoma treated by adjuvant cytotoxic chemotherapy after surgical resection, with a 5-year survival. There is no specific chemotherapy for malignant pheochromocytoma, but because it has the same embryologic origin as neuroblastoma, we used similar chemotherapy. Because of unexpected malignancy potential, we think that total and meticulous resection of the tumor must be done.
我们报告了一例原发性恶性心脏嗜铬细胞瘤的病例，该患者在手术切除后接受了辅助细胞毒性化疗，存活了5年。目前尚无针对恶性嗜铬细胞瘤的特异性化疗方法，但由于其与神经母细胞瘤具有相同的胚胎学起源，我们采用了类似的化疗方案。鉴于其意外的恶性潜能，我们认为必须对肿瘤进行完整且细致的切除。
