与X连锁淋巴增殖性疾病相关的免疫缺陷性支气管扩张症。
Immune-deficient bronchiectasis associated with X-linked lymphoproliferative disease.
作者信息
Mehta V K, Massad M G, Tripathi S P, Koshy M, Geha A S
机构信息
Division of Cardiothoracic Surgery, University of Illinois at Chicago, 60612, USA.
出版信息
Ann Thorac Surg. 1999 Aug;68(2):578-80. doi: 10.1016/s0003-4975(99)00603-7.
Abstract
Bronchiectasis may occur with various congenital and acquired immunodeficiency diseases. The association of bronchiectasis and the X-linked lymphoproliferative disease (XLP), also known as Duncan's disease is unknown. We describe the case of a 39-year-old man with XLP, the oldest surviving, who developed chronic bronchiectasis with hemoptysis and required a pneumonectomy to control his symptoms.
摘要
支气管扩张可能与多种先天性和获得性免疫缺陷疾病有关。支气管扩张与X连锁淋巴增殖性疾病（XLP）（也称为邓肯病）之间的关联尚不清楚。我们描述了一例39岁患有XLP的男性病例，他是存活时间最长的患者，出现了伴有咯血的慢性支气管扩张，需要进行肺切除术来控制症状。
Zotero 插件