上颌骨恶性外周神经鞘瘤伴冯雷克林霍增氏病
Malignant peripheral nerve sheath tumour in the maxilla associated with von Recklinghausen's disease.
作者信息
Muraki Y, Tateishi A, Tominaga K, Fukuda J, Haneji T, Iwata Y
机构信息
First Department of Oral and Maxillofacial Surgery, Kyushu Dental College, 2-6-1 Manazuru, Kokurakita-ku, Kitakyushu 803.
出版信息
Oral Dis. 1999 Jul;5(3):250-2. doi: 10.1111/j.1601-0825.1999.tb00310.x.
Malignant transformation of neurofibromatosis is one of the most serious complications of von Recklinghausen's disease (VRD). The most common associated malignancy is the malignant peripheral nerve sheath tumour (MPNST). Few cases of MPNST associated with VRD in the maxillary region have been reported. This report describes a rare case of MPNST in the maxilla and the aggressive nature of MPNST associated with VRD.
神经纤维瘤病的恶性转化是冯雷克林霍增氏病（VRD）最严重的并发症之一。最常见的相关恶性肿瘤是恶性外周神经鞘瘤（MPNST）。上颌区域与VRD相关的MPNST病例报道较少。本报告描述了一例罕见的上颌MPNST病例以及与VRD相关的MPNST的侵袭性。
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