Guyot-Drouot M H, Cotten A, Flipo R M, Lecomte Houcke M, Delcambre B
Rheumatology Department, R. Salengro Teaching Hospital, Lille, France.
Rev Rhum Engl Ed. 1999 Oct;66(10):516-9.
A case of extraskeletal Ewing's sarcoma presenting as a large gluteal mass is reported. This is a rare tumor with a frequently grim prognosis. Although the definitive diagnosis requires histological examination, magnetic resonance imaging is useful for determining the location of the tumor, evaluating its spread, and eliminating skeletal Ewing's sarcoma by establishing the integrity of the neighboring bone marrow. The tumor is seen on T1-weighted images as low signal with heterogeneous postgadolinium enhancement. Signal intensity on T2-weighted images is variable. In the case reported here, combination chemotherapy with external beam radiation therapy was ineffective, and the patient died 12 months after the diagnosis.
报告了一例表现为巨大臀肌肿块的骨外尤因肉瘤病例。这是一种罕见肿瘤，预后通常较差。尽管明确诊断需要组织学检查，但磁共振成像有助于确定肿瘤位置、评估其扩散情况，并通过确定邻近骨髓的完整性排除骨尤因肉瘤。在T1加权图像上，肿瘤表现为低信号，钆增强后不均匀强化。T2加权图像上的信号强度各不相同。在此报告的病例中，联合化疗及外照射放疗无效，患者在诊断后12个月死亡。
