Salooja N, Martin P, Khair K, Liesner R, Hann I
Great Ormond Street Hospital for children, London, UK.
Haemophilia. 2000 Jan;6(1):44-6. doi: 10.1046/j.1365-2516.2000.00362.x.
We report a case of severe factor V (FV) deficiency (<1%) associated with multiple episodes of intracranial bleeding which presented at birth. The clinical course was further complicated by the development of an inhibitor, episodes of sepsis and cardiac failure. The management using virally inactivated FFP and platelets is discussed.
我们报告了一例出生时即出现严重因子V(FV)缺乏(<1%)并伴有多次颅内出血的病例。临床病程因抑制剂的出现、败血症发作和心力衰竭而进一步复杂化。文中讨论了使用病毒灭活新鲜冰冻血浆和血小板的治疗方法。