Ling F T, David T E, Merchant N, Yu E, Butany J W
Department of Laboratory Medicine and Pathobiology, Toronto General Hospital, University of Toronto, Ontario, Canada.
Can J Cardiol. 2000 Jan;16(1):73-9.
Intravenous leiomyomatosis is an uncommon clinical entity characterized by the growth of a benign, smooth muscle tumour within the venous system. Intracardiac extension of this tumour is rare, and approximately 35 cases have been reported in the literature. The second case of massive intracardiac extension of intravenous leiomyomatosis is reported in a pregnant patient diagnosed after the unusual presentation of seizure activity. Tumours were successfully removed from the right internal iliac vein, inferior vena cava, and right atrium and ventricle in a single-stage operation using cardiopulmonary bypass and circulatory arrest. Concomitant total abdominal hysterectomy and bilateral salpingo-oophorectomy were performed. Nine months after diagnosis, the patient was evaluated for recurrent disease. A review of the literature from 1994 to 1998 is presented.
静脉内平滑肌瘤病是一种罕见的临床病症，其特征为在静脉系统内生长良性平滑肌肿瘤。这种肿瘤向心腔内延伸的情况罕见，文献中报道了约35例。本文报道了第二例静脉内平滑肌瘤病大量向心腔内延伸的病例，该病例为一名孕妇，在出现癫痫发作这一不寻常表现后被确诊。通过体外循环和循环停止，在一期手术中成功地从右髂内静脉、下腔静脉以及右心房和心室切除了肿瘤。同时进行了全腹子宫切除术和双侧输卵管卵巢切除术。诊断后九个月，对该患者进行了复发性疾病评估。并呈现了1994年至1998年的文献综述。
