Fujimoto Y, Aguiar P H, Carneiro J D, Martins R S, Ciquini O, de Andrade A F, Manreza L A
University of São Paulo School of Medicine, Brazil.
Neurosurg Rev. 1999 Dec;22(4):226-9. doi: 10.1007/s101430050022.
The authors describe a case of an infant with congenital factor X deficiency. The patient presented with a central nervous system hemorrhage followed by hydrocephalus. He underwent a ventriculoperitoneal shunt and, during the postoperative period, developed a spontaneous epidural hematoma, which was evacuated. The clinical and pathophysiological aspects of this case are discussed based on a literature review.
作者描述了一例先天性因子X缺乏症婴儿的病例。该患者出现中枢神经系统出血,随后发展为脑积水。他接受了脑室腹腔分流术,术后出现自发性硬膜外血肿,并进行了血肿清除术。基于文献综述讨论了该病例的临床和病理生理学方面。