Calatrava L, Donado M
J Maxillofac Surg. 1976 Dec;4(4):238-41. doi: 10.1016/s0301-0503(76)80045-8.
This report describes the case of a 2-year-old girl with desmoplastic fibroma of the mandible, with swelling in the region of the mandibular angle which had been wrongly diagnosed several times. A biopsy was interpreted as showing a low-grade fibrosarcoma. The patient then received treatment with cytotoxic drugs, and later a mandibular hemi-resection was performed. The postoperative diagnosis was Jaffé's desmoplastic fibroma (non-osteogenic). The age of the patient, the rapid development of the tumour and the accompanying pain suggested a sarcoma, and the first pathological examination seemed to provide confirmation. The post-operative course was very favorable, and the patient is considered to clinically cured, after one year.
本报告描述了一名2岁女童下颌骨促结缔组织增生性纤维瘤的病例，该患儿下颌角区域肿胀，曾被多次误诊。活检结果被解读为低级别纤维肉瘤。该患者随后接受了细胞毒性药物治疗，之后进行了下颌骨半切除术。术后诊断为贾菲促结缔组织增生性纤维瘤（非成骨性）。患者的年龄、肿瘤的快速发展以及伴随的疼痛提示为肉瘤，首次病理检查似乎也证实了这一点。术后病程非常顺利，一年后该患者被认为已临床治愈。
