Labouré S, Besson R, Lamblin M D, Debeugny P
Department of Paediatric Surgery, Jeanne de Flandres Hospital, University of Lille, France.
Eur J Pediatr Surg. 2000 Feb;10(1):23-9. doi: 10.1055/s-2008-1072318.
Low anorectal malformations are considered to be a benign type of anorectal malformations. Their treatment is simple in the neonatal period and gives good results as far continence is concerned.
We studied a group of 55 boys with low anorectal malformations which had been surgically treated between the 1st January 1975 and the 31st December 1992. We studied the initial treatment and the associated anomalies, 5 patients have died. 27 were seen for an interview and a clinical examination. Extra investigations (anorectal manometry or electromyography of external sphincter) were only offered to consenting patients with an ongoing problem.
3 to 20 years had passed since their operations. Associated anomalies had been found in 11 children. The initial treatment was a perineal procedure in 20 cases and a colostomy in 8 cases. Dilatations were carried out on 11 children. Faecal and urinary continence had been acquired before 30 months of age. 13 children (48%) had problems of soiling and/or chronic constipation. There was no difference between these children and the 14 continent ones regarding the type of malformation, the initial treatment and the follow-up. Anorectal manometry (performed on 9 cases) showed 4 anorectal dyssynergies. It was normal in 3 cases. The Recto Anal Inhibitory Reflex was always present.
Problems of continence are not rare in the evolution of low anorectal malformations. We suggest therefore a long-term clinical follow-up for those children, with one anorectal manometry control being performed after continence is acquired.
低位肛门直肠畸形被认为是肛门直肠畸形的一种良性类型。其在新生儿期的治疗简单,就控便情况而言效果良好。
我们研究了一组55名患有低位肛门直肠畸形的男孩,他们于1975年1月1日至1992年12月31日期间接受了手术治疗。我们研究了初始治疗及相关畸形情况,5例患者死亡。27例接受了访谈和临床检查。仅对有持续问题且同意的患者进行了额外检查(肛门直肠测压或外括约肌肌电图检查)。
自手术以来已过去3至20年。11名儿童发现有相关畸形。初始治疗中,20例行会阴手术,8例行结肠造口术。11名儿童进行了扩张治疗。30个月龄前已实现粪便和尿液自控。13名儿童(48%)存在污粪和/或慢性便秘问题。这些儿童与14名控便正常的儿童在畸形类型、初始治疗及随访方面无差异。9例进行了肛门直肠测压,其中4例存在肛门直肠协同失调,3例正常。直肠肛门抑制反射始终存在。
在低位肛门直肠畸形的发展过程中,控便问题并不罕见。因此,我们建议对这些儿童进行长期临床随访,在实现控便后进行一次肛门直肠测压检查。