Rarivomanana M, Vololonantenaina C R, Valikara S, Rakotomanga P, Randrianasolo O, Chouteau Y
Service de chirurgie, CHR de Toliara, Madagascar.
Bull Soc Pathol Exot. 2000 Feb;93(1):29-30.
Rhabdomyosarcomas are the most common sarcomas of the soft tissues found in children under 15 years. The reported observation is of a vaginal tumour having developed in an eleven-month-year-old little girl. It was a typical botryoid rhabdomyosarcoma, usually found in the hollow organs surrounded on the edges by mucus. Rhabdomyosarcomas have many characteristics which vary greatly according to the degree of their cellular differenciation. The majority of these tumours can be classified into four histological categories: embryonic, botryoid, alveolar or plemorphous. The treatment is exeresis surgery with radio- and chemotherapy. Prognosis, however, remains dim despite the therapeutic advances of the last few years.
横纹肌肉瘤是15岁以下儿童中最常见的软组织肉瘤。据报道,一名11个月大的小女孩阴道出现了肿瘤。这是典型的葡萄状横纹肌肉瘤,通常发生在边缘被黏液包围的中空器官中。横纹肌肉瘤有许多特征,根据其细胞分化程度差异很大。这些肿瘤大多数可分为四种组织学类型:胚胎型、葡萄状、肺泡型或多形型。治疗方法是手术切除并结合放疗和化疗。然而,尽管过去几年治疗有进展,但预后仍然不佳。