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产前检测到多个心脏横纹肌瘤。

Multiple cardiac rhabdomyomas detected in utero.

作者信息

Choi J M, Jaffe R, Maidman J, Baxi L V

机构信息

Department of Obstetrics and Gynecology, Sloane Hospital for Women at New York Presbyterian Hospital, Columbia University, New York, NY 10032, USA.

出版信息

Fetal Diagn Ther. 2000 May-Jun;15(3):174-6. doi: 10.1159/000021000.

DOI:10.1159/000021000
PMID:10782004
Abstract

Prenatal fetal echocardiography studies detected large multiple cardiac rhabdomyomas and led to the diagnosis of tuberous sclerosis. Despite episodes of bradyarrhythmias and severe lung compression in utero, the neonate did well and was discharged home on day 20 of life. On day 30 of life, the infant expired at home from cardiac arrest secondary to arrhythmia.

摘要

产前胎儿超声心动图检查发现多个巨大心脏横纹肌瘤,从而诊断为结节性硬化症。尽管胎儿在子宫内出现过缓慢性心律失常和严重肺受压情况,但新生儿情况良好,于出生后第20天出院回家。出生后第30天,婴儿在家中因心律失常继发心脏骤停而死亡。

相似文献

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Multiple cardiac rhabdomyomas detected in utero.产前检测到多个心脏横纹肌瘤。
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引用本文的文献

1
[Multiple cardiac rhabdomyomas, prenatal diagnosis. Case report].[多发性心脏横纹肌瘤,产前诊断。病例报告]
Arch Cardiol Mex. 2022 Jan 3;92(1):94-98. doi: 10.24875/ACM.200002031.
2
Fetal arrhythmias associated with cardiac rhabdomyomas.胎儿心律失常与心脏横纹肌瘤相关。
Heart Rhythm. 2014 Apr;11(4):677-83. doi: 10.1016/j.hrthm.2013.12.018. Epub 2013 Dec 11.
3
Ventricular tachycardia in a neonate with prenatally diagnosed cardiac tumors: a case with tuberous sclerosis.产前诊断为心脏肿瘤的新生儿室性心动过速:1例结节性硬化症病例
Pediatr Cardiol. 2005 Sep-Oct;26(5):655-7. doi: 10.1007/s00246-004-0714-5.
4
Cardiac rhabdomyoma and tuberous sclerosis: prenatal diagnosis and follow-up.心脏横纹肌瘤与结节性硬化症:产前诊断与随访
Indian J Pediatr. 2003 Jan;70(1):87-9. doi: 10.1007/BF02722750.