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Congenital Heart Surgery Nomenclature and Database Project: pediatric cardiomyopathies and end-stage congenital heart disease.

作者信息

Delius R E

机构信息

Division of Cardiothoracic Surgery, University of California, Davis School of Medicine, Sacramento 95817, USA.

出版信息

Ann Thorac Surg. 2000 Apr;69(4 Suppl):S180-90. doi: 10.1016/s0003-4975(99)01243-6.

DOI:10.1016/s0003-4975(99)01243-6
PMID:10798428
Abstract

The extant nomenclature for cardiomyopathy is reviewed for the purpose of establishing a unified reporting system. The subject was debated and reviewed by members of the STS-Congenital Heart Surgery Database Committee and representatives from the European Association for Cardiothoracic Surgery. All efforts were made to include all relevant nomenclature categories using synonyms where appropriate. A functional classification based on pathophysiology is proposed. Cardiomyopathy is subdivided into: dilated cardiomyopathy, hypertrophic cardiomyopathy, restrictive cardiomyopathy, right ventricular cardiomyopathy, and end-stage congenital heart disease. A comprehensive database set is presented that is based on a hierarchical scheme. Data are entered at various levels of complexity and detail that can be determined by the clinician. These data can lay the foundation for comprehensive risk stratification analyses. A minimum database set is also presented that will allow for data sharing and would lend itself to basic interpretation of trends. Outcome tables relating diagnoses, procedures, and various risk factors are presented.

摘要

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