Bodova I, Horakova J, Lukac J, Cupanikova D, Plank L
Bratisl Lek Listy. 2000;101(1):54-6.
The authors describe a case report of a six months old boy with autoimmune hemolytic anemia and giant cell hepatitis. This is a very rare syndrome in infancy. After eleven months of intensive immunosuppressive treatment (glucocorticoids, cyclosporin A, azathioprin, intravenous immunoglobulins, cyclophosphamid) no improvement of hemolysis was observed and therefore splenectomy was indicated. 1 year after the treatment was finished the patient is in good general condition and his hematologic and biochemical parameters are physiological.
作者描述了一例患有自身免疫性溶血性贫血和巨细胞肝炎的6个月大男孩的病例报告。这在婴儿期是一种非常罕见的综合征。经过11个月的强化免疫抑制治疗(糖皮质激素、环孢素A、硫唑嘌呤、静脉注射免疫球蛋白、环磷酰胺),未观察到溶血情况有所改善,因此建议进行脾切除术。治疗结束1年后,患者总体状况良好,血液学和生化指标均正常。