Akcoral A, Oran B, Tavli V, Oren H, Cevik N T
Division of Cardiology, Dokuz Eylul University School of Medicine, Izmir, Turkey.
Indian J Pediatr. 1996 Sep-Oct;63(5):700-3. doi: 10.1007/BF02730827.
Hypertrophic cardiomyopathy (HCM) is a rare primary myocardial disease, characterized by hypertrophy of the left and/or right ventricle. Infants of diabetic mothers (IDM) are at risk for development of HCM, respiratory distress and persistent pulmonary hypertension. A case of severe right sided HCM in an infant born to a diabetic mother is presented. The patient's findings were complementary to the previous observations reporting HCM in IDM. The presence of disproportionate septal hypertrophy in the echocardiography of an infant born to a diabetic mother is highly suggestive of HCM in IDM. In our opinion, further cardiac evaluation is not indicated unless other cardiac abnormalities are suspected.
肥厚型心肌病(HCM)是一种罕见的原发性心肌疾病,其特征为左心室和/或右心室肥厚。糖尿病母亲的婴儿(IDM)有患HCM、呼吸窘迫和持续性肺动脉高压的风险。本文报告了一例糖尿病母亲所生婴儿患严重右心室HCM的病例。该患者的检查结果补充了先前关于IDM患HCM的观察报告。糖尿病母亲所生婴儿的超声心动图显示有不成比例的室间隔肥厚,这强烈提示IDM患HCM。我们认为,除非怀疑有其他心脏异常,否则无需进一步进行心脏评估。