Tongue reduction in Beckwith-Weidemann syndrome.

OBJECTIVE

To review our experience with patients with macroglossia as a component of Beckwith-Weidemann Syndrome (BWS).

DESIGN

Chart review of six patients treated with BWS.

SETTING

Tertiary care teaching hospital.

PATIENTS

Six patients diagnosed with BWS and macroglossia.

INTERVENTIONS

Four patients underwent at least one surgical procedure to address their macroglossia. The surgical options and potential complications are discussed.

RESULTS

Three patients who have undergone tongue reduction have a functioning tongue with normal mobility. Two patients have required tracheotomy as apart of their management and still have significant tongue enlargement.

CONCLUSIONS

Macroglossia as a part of BWS may present a difficult management problem. Various methods of tongue reductions have been reported with mixed results.