Fignon A, Marret H, Body G, Saile N, Lanson Y, Le Floch O, Fetissof F
Département de Gynécologie Obstétrique, Biologie de la Reproduction et Médecine Faetale, CHU Bretonneau, Tours.
Ann Chir. 1997;51(9):1023-7.
Malignant fibrous histiocytoma is the commonest soft tissue sarcoma of adults. The soft tissue of the extremities is the commonest primary site of malignant fibrous histiocytoma. It is much less common in the female retroperitoneum, leading to diagnostic errors. The clinical, radiographic and CT signs are non-specific. This tumor can only be diagnosed by histology. An initial complete resection is essential for successful treatment of the primary tumor. Radiation therapy is limited and chemotherapy has only been successful in a limited number of cases. This tumor has a poor prognosis. These lesions are relatively rare and consequently difficult to study. The authors report three cases and review the literature.
恶性纤维组织细胞瘤是成人最常见的软组织肉瘤。四肢软组织是恶性纤维组织细胞瘤最常见的原发部位。它在女性腹膜后较少见,容易导致诊断错误。其临床、影像学和CT表现均无特异性。该肿瘤只能通过组织学诊断。对于原发性肿瘤的成功治疗,初次完整切除至关重要。放射治疗效果有限,化疗仅在少数病例中取得成功。这种肿瘤预后较差。这些病变相对罕见,因此难以研究。作者报告了三例病例并复习了文献。