Vergoz D, Warlin J F, Salat J, Le Lorier G
Phlebologie. 1976 Jan-Mar;29(1):33-7.
Giant haemangiomas combined with a haemostasis disorder of the Kasabach-Meritt type are rare and even more rare are the problems posed during labour when vulvo-vagino-uterine sites are involved. Two cases are reported. After summary of the clinical and biochemical studies, the authors report attempts to improve the haemostasis disorder, first with heparin and then with antifibrinolytic preparations, and to improve the angiomas with antifibrinolytic preparations in the hope of stimulating intrasacular thrombosis. In particular, the obstetric and surgical problems are discussed in the context of labour. In one case the outcome of labour was successful only moderate transfusion being required, and in the other the outcome was fatal despite the use of about 100 bottles of blood in the first 24 hours. In both cases the infants were normal.
巨大血管瘤合并卡萨巴赫 - 梅里特型止血障碍十分罕见，而累及外阴 - 阴道 - 子宫部位时，分娩期间出现的问题更是罕见。本文报告了两例病例。在总结临床和生化研究后，作者报告了改善止血障碍的尝试，先是使用肝素，然后使用抗纤溶制剂，并用抗纤溶制剂改善血管瘤，以期刺激血管内血栓形成。特别在分娩背景下讨论了产科和外科问题。一例分娩成功，仅需适度输血；另一例尽管在最初24小时内使用了约100瓶血液，结局仍为死亡。两例中的婴儿均正常。
