Imamura H, Momose T, Kitabayashi H, Takahashi W, Yazaki Y, Takenaka H, Isobe M, Sekiguchi M, Kubo K
The First Department of Internal Medicine, Shinshu University School of Medicine, Matsumoto, Japan.
Jpn Circ J. 2000 Jun;64(6):471-3. doi: 10.1253/jcj.64.471.
This report describes a patient with severe pulmonary hypertension accompanied by a congenital intrahepatic portosystemic shunt. Primary pulmonary hypertension was suspected initially because none of the classic symptoms of a portosystemic shunt were present. Physicians should note that disorders of the portal system may cause pulmonary hypertension even in the absence of symptoms suggesting liver disease.
本报告描述了一名患有严重肺动脉高压并伴有先天性肝内门体分流的患者。最初怀疑是原发性肺动脉高压，因为不存在门体分流的典型症状。医生应注意，即使没有提示肝脏疾病的症状，门脉系统疾病也可能导致肺动脉高压。
