Schena S, Caniglia A, Agnino A, Caruso G, Ferlan G
Institute of Cardiac Surgery, Institute of Pathology, Medical School, University of Bari, Italy.
Chest. 2000 Jul;118(1):271-3. doi: 10.1378/chest.118.1.271.
The authors report the successful surgical and chemotherapeutic management of a malignant fibrous histiocytoma with localization in the heart. This rare malignancy has specific morphologic characteristics and is diagnosed in adults when it is already locally aggressive or metastasized. The average survival time for patients with malignant fibrous histiocytoma is < 12 months. Neither clinical nor instrumental signs of recurrence have been detected in this patient after an aggressive surgical resection and a specific therapeutic approach.
作者报告了1例心脏恶性纤维组织细胞瘤的成功手术及化疗治疗。这种罕见的恶性肿瘤具有特定的形态学特征，在成人中被诊断时通常已具有局部侵袭性或发生转移。恶性纤维组织细胞瘤患者的平均生存时间<12个月。在积极的手术切除和特定的治疗方法后，该患者未检测到复发的临床或影像学迹象。
