Leinung S, Lotz I, Würl P, Frey A, Lochhaas L, Schönfelder M
Chirurgische Klinik I, Universität Leipzig.
Rontgenpraxis. 2000;52(9):302-8.
The venal haemangioma is defined as a benign tumor consisting of veinlike vessels. The preoperative diagnosis and its inherent problems are illustrated using a coincidentally diagnosed monstrous haemangioma tumor of the retroperitonial space in a twenty year old patient. With respect to our patient, X-ray, computer tomography and angiography all failed as diagnostic tools. Only the use of Doppler sonographic flow signals suggested the presence of a haemangioma. The morphology, prognosis and clinical significance of blood vessel tumors are multifaceted. The most important differential diagnoses to the venous haemangioma are the cavernous and the capilliary haemangioma. The venous haemangioma distinguishes itself through the presence of blood vessel walls. Haemangiomas are common benign tumors. In the presence of highly developed muscular components, there exists a transition to angiomyomas and to leiomyomas. Venal haemangiomas are extremely rare in the demonstrated localisation of the retroperitoneal space. Here they can grow to monstrous preportions whilst remaining undetected. Thus the patient is under the potential danger of bleeding to death through trivial injuries. The therapy of choice remains total surgical excision. In situations of unclear clinical results with respect to preoperative diagnosis especially amongst young adults, one should at least consider the possibility of a haemangioma as the root of the problem.
静脉血管瘤被定义为一种由静脉样血管构成的良性肿瘤。通过一位20岁患者腹膜后间隙偶然诊断出的巨大血管瘤病例,阐述了术前诊断及其内在问题。就我们的患者而言,X线、计算机断层扫描和血管造影作为诊断工具均告失败。只有使用多普勒超声血流信号提示存在血管瘤。血管肿瘤的形态、预后和临床意义是多方面的。静脉血管瘤最重要的鉴别诊断是海绵状血管瘤和毛细血管血管瘤。静脉血管瘤通过血管壁的存在而得以区分。血管瘤是常见的良性肿瘤。在存在高度发达的肌肉成分时,会向血管肌瘤和平滑肌瘤转变。静脉血管瘤在腹膜后间隙所示的部位极其罕见。在此处它们可生长到巨大规模而仍未被发现。因此,患者面临因轻微损伤而出血致死的潜在危险。首选的治疗方法仍然是完全手术切除。在术前诊断临床结果不明确的情况下,尤其是在年轻人中,至少应考虑血管瘤作为问题根源的可能性。