Mohan J C, Passey R, Arora R
Department of Cardiology, G.B. Pant Hospital, 110002, New Delhi,
Int J Cardiol. 2000 Jul 31;74(2-3):153-7. doi: 10.1016/s0167-5273(00)00263-1.
A series of nine consecutive patients with unguarded tricuspid valve orifice as a result of partial or complete agenesis of the valvar tissue and patent right ventricular outflow tract is reported. Clinical manifestations were cyanosis, severe right ventricular failure and incidental echocardiographic detection in a young patient with dilated cardiomyopathy. This series contains the oldest reported patient with this malady, who was misdiagnosed as portal hypertension for 10 years. This study, with possibly the largest number of patients reported so far, sheds some light on the natural history of a rare entity.
报告了一系列连续9例患者，这些患者因瓣膜组织部分或完全发育不全以及右心室流出道通畅而存在无保护的三尖瓣口。临床表现为发绀、严重右心衰竭，在一名患有扩张型心肌病的年轻患者中通过超声心动图偶然发现。该系列包含了报道中患有这种疾病的最年长患者，该患者被误诊为门静脉高压达10年之久。这项研究报告的患者数量可能是迄今为止最多的，为这一罕见病症的自然病史提供了一些线索。
