Takahira K, Ohi S, Fujii N, Matsuura Y, Sano M, Hanai H, Kaneko E
Department of Gastroenterology, Yaizu Municipal General Hospital, Japan.
J Gastroenterol. 2000;35(9):712-6. doi: 10.1007/s005350070052.
Intra-abdominal desmoplastic small round cell tumor (IDSRT) is a rare neoplasm that develops in the abdominal cavity in young people. We experienced a 27-year-old man who visited with ascites of unknown cause. Compression of the colon was found by barium enema examination. On colonoscopic examination, diffuse white elevated lesions, about 5 mm in diameter, surrounded by rubedo, so-called aphthoid lesions, were also observed. IDSRT was diagnosed by biopsy at laparotomy, and chemotherapy with cyclophosphamide, etoposide, doxorubicin, and cisplatin was performed. The tumors shrank temporarily (partial response), but subsequently grew in size again. The patient died during the second course of chemotherapy after relapse. We present one case report, together with a review of the literature.
腹腔促结缔组织增生性小圆细胞肿瘤（IDSRT）是一种罕见的肿瘤，发生于年轻人的腹腔。我们遇到一名27岁男性，因不明原因腹水前来就诊。钡灌肠检查发现结肠受压。结肠镜检查时，还观察到弥漫性白色隆起病变，直径约5毫米，周围有红斑，即所谓的口疮样病变。剖腹手术活检诊断为IDSRT，并采用环磷酰胺、依托泊苷、阿霉素和顺铂进行化疗。肿瘤暂时缩小（部分缓解），但随后再次增大。患者在复发后的第二个化疗疗程中死亡。我们报告1例病例，并对文献进行综述。
