Mayuzumi H, Kato T, Aida T, Sato N, Sawamura Y
Departoment of Neurosurgery, Hakodate Central Hospital, Japan.
No Shinkei Geka. 2000 Sep;28(9):797-802.
Epidermoids known as cholesteatomas, are congenital benign tumors and originate in the embryonic ectoderm. They account for 1.3% of all intracranial tumors. They are often found in the cerebellopontine angle and the paraseller region, but rarely in the petrous portion of the temporal bone. Epidermoids of the petrous bone tend to slowly present progressive facial palsy and hearing disturbance. In this article, two cases of epidermoids involving the petrous bone are reported. A 55-year-old male presented left facial palsy, left hearing disturbance and decreased gustation in the left side of the tongue. MRI revealed a non-enhanced mass on the petrous portion of the left temporal bone, and bone-window CT showed bone destruction in the same region (Case 1). A 71-year-old female was aware of left facial palsy and left hearing loss for 15 years. MRI showed a non-enhanced mass on the petrous bone, and bone-window CT demonstrated extensive bone erosion of the petrous bone and the middle cranial fossa (Case 2). In both cases, total removal was performed via the middle cranial fossa approach. Both tumors existed extradurally and had pressed against the genicurate ganglion of the facial nerve. The facial palsy of the former case recovered 12 months after surgery. We discuss the problems of diagnosis and treatment of epidermoids of the petrous bone.
表皮样囊肿又称胆脂瘤,是先天性良性肿瘤,起源于胚胎外胚层。它们占所有颅内肿瘤的1.3%。常发现于桥小脑角和鞍旁区域,但很少见于颞骨岩部。岩部表皮样囊肿往往会缓慢出现进行性面瘫和听力障碍。本文报告2例累及岩部的表皮样囊肿。1例55岁男性,出现左侧面瘫、左侧听力障碍及左侧舌味觉减退。MRI显示左侧颞骨岩部有一不强化肿块,骨窗CT显示同一区域骨质破坏(病例1)。另1例71岁女性,15年来一直存在左侧面瘫和左耳听力丧失。MRI显示岩部有一不强化肿块,骨窗CT显示岩部和中颅窝广泛骨质侵蚀(病例2)。两例均经中颅窝入路行肿瘤全切除。两例肿瘤均位于硬膜外,压迫面神经膝状神经节。前1例患者术后12个月面瘫恢复。我们讨论了岩部表皮样囊肿的诊断和治疗问题。