对一名患有扩张型心肌病的3岁男孩实施部分左心室切除术。

Partial left ventriculectomy in a 3-year-old boy with dilated cardiomyopathy.

作者信息

Osawa H, Yoshii S, Hosaka S, Suzuki S, Kaga S, Tada Y

机构信息

Department of Surgery, Yamanashi Medical University, Japan.

出版信息

Jpn J Thorac Cardiovasc Surg. 2000 Sep;48(9):590-3. doi: 10.1007/BF03218207.

DOI:10.1007/BF03218207

PMID:11030133

Abstract

A 3-year-old boy suffered severe heart failure 2 months after ventricular septal defect repair. The cardiothoracic ratio was 67% and the ejection fraction 13%. Echocardiography showed a dilated left ventricle and thin myocardium. After thorough study, we made a diagnosis of dilated cardiomyopathy. Because conventional therapy was unsuccessful, we conducted partial left ventriculectomy with Alfieri repair of the mitral valve. The postoperative cardiothoracic ratio was 57% at 1 year of follow-up and the ejection fraction 40%. The New York Heart Association functional class improved from IV to I. In conclusion, the role of partial left ventriculectomy is both as a bridge to transplantation and as a definitive repair in dilated cardiomyopathy during childhood.

摘要

一名3岁男孩在室间隔缺损修复术后2个月出现严重心力衰竭。心胸比率为67%，射血分数为13%。超声心动图显示左心室扩张，心肌变薄。经过全面检查，我们诊断为扩张型心肌病。由于传统治疗方法未成功，我们进行了部分左心室切除术并采用阿尔菲里二尖瓣修复术。随访1年时，术后心胸比率为57%，射血分数为40%。纽约心脏协会心功能分级从IV级改善到I级。总之，部分左心室切除术在儿童扩张型心肌病中既作为移植的桥梁，也作为确定性修复方法。