Ziyeh S, Berger R, Reisner K
Radiologische Klinik, St. Vincentiuskrankenhäuser, Karlsruhe, Germany.
Eur Radiol. 2000;10(10):1675-7. doi: 10.1007/s003300000429.
Osteogenesis imperfecta (OI) is an inherited generalized disorder of type-I collagen synthesis often associated with hearing loss. We present a case of OI type I in which hearing loss led to examination of the temporal bone with MRI. In the osseous otic capsule MRI demonstrated pericochlear lesions with soft tissue signal intensity and contrast enhancement. Changes similar to otosclerosis have been described in the temporal bone of OI patients when applying CT, but reports on MRI findings do not yet exist.
成骨不全症（OI）是一种遗传性的I型胶原蛋白合成全身性疾病，常伴有听力损失。我们报告一例I型成骨不全症病例，该病例中听力损失促使通过MRI对颞骨进行检查。在骨性听骨囊中，MRI显示耳蜗周围病变，具有软组织信号强度并伴有对比增强。应用CT检查时，OI患者的颞骨中已发现类似耳硬化症的变化，但尚无关于MRI检查结果的报告。
