Borg S A, Young L W, Roghair G D
Am J Roentgenol Radium Ther Nucl Med. 1975 Oct;125(2):412-21. doi: 10.2214/ajr.125.2.412.
Some cardiovascular lesions may result in tracheobronchial obstruction and many of these will commonly be associated with infantile lobar emphysema (ILE). By contrast a relatively smaller percentage of cases of ILE results from vascular compression. We offer a new term, "congenital avalvular pulmonary artery (CAPA)," to describe the complex of the absent pulmonary valve and the concomitant marked pulmonary artery dilatation because CAPA is more descriptively inclusive of the abnormality of the artery beyond the valve. The diagnostic correlation of CAPA and ILE is of considerable importance since the initial presentation of CAPA is usually as ILE and the recognition of a triangular or rounded hilar density should raise suspicion for CAPA even before clinical signs become evident. Differential diagnosis must include other causes of ILE including infantile lobar emphysema with bronchial atresia.
一些心血管病变可能导致气管支气管阻塞，其中许多通常与婴儿大叶性肺气肿（ILE）相关。相比之下，ILE病例中由血管压迫导致的比例相对较小。我们提出一个新术语“先天性无瓣肺动脉（CAPA）”，用于描述肺动脉瓣缺失及伴随的显著肺动脉扩张这一复合体，因为CAPA更具描述性地涵盖了瓣膜远端动脉的异常。CAPA与ILE的诊断关联至关重要，因为CAPA最初通常表现为ILE，即使在临床体征明显之前，识别出三角形或圆形肺门密度也应引起对CAPA的怀疑。鉴别诊断必须包括ILE的其他病因，包括伴有支气管闭锁的婴儿大叶性肺气肿。
