Soylu H, Koltuksuz U, Kutlu N O, Sarihan H, Sen Y, Ustün N, Baki A, Sönmezgöz E, Dogrul M, Akinci A
Department of Pediatrics, Inönü University, Turgut Ozal Medical Center, Malatya, Turkey.
Pediatr Pulmonol. 2000 Nov;30(5):429-33. doi: 10.1002/1099-0496(200011)30:5<429::aid-ppul10>3.0.co;2-h.
Morgagni hernia (MH) is the least common type of congenital diaphragmatic hernias. Although its course is often asymptomatic, it may be associated with various respiratory and gastrointestinal symptoms. We describe 7 children with MH during a 5-year period in three pediatric centers in Turkey. All children had acute or chronic respiratory symptoms; cough was the most frequent. The diagnosis was made by posterior-anterior (PA) and lateral chest X-rays. The PA chest X-rays showed a homogenous mass in 2 and a gas-filled cystic image in 3 children in the right cardiophrenic angle. A retrocardiac homogeneous density in one child, and bilateral consolidation in lower lung areas in another child were also seen. All lateral chest X-rays showed gas-filled bowel loops above the diaphragm. The diagnosis was confirmed by barium-contrast radiograph. Four patients had five additional anomalies, i.e., ventricular septal defect, right inguinal hernia, congenital hip dislocation, pectus carinatum, and obstruction of the uretero-pelvic junction. All of the hernias were repaired by an abdominal approach. There were no complications or recurrences during follow-up. In conclusion, MH should be considered in the differential diagnosis of cases of long-standing respiratory symptoms and/or when an unexplained radiological image, especially on the right cardiophrenic area, is present.
莫尔加尼疝(MH)是先天性膈疝中最不常见的类型。尽管其病程通常无症状,但可能与各种呼吸和胃肠道症状相关。我们描述了土耳其三个儿科中心在5年期间的7例莫尔加尼疝患儿。所有患儿均有急性或慢性呼吸道症状;咳嗽最为常见。通过后前位(PA)和侧位胸部X线片进行诊断。PA胸部X线片显示,2例患儿右心膈角有均匀肿块,3例患儿有充气的囊性影像。还可见1例患儿心后区均匀密度影,另1例患儿下肺野双侧实变。所有侧位胸部X线片均显示膈上有充气的肠袢。通过钡剂造影X线片确诊。4例患儿还有另外5种异常,即室间隔缺损、右侧腹股沟疝、先天性髋关节脱位、鸡胸和输尿管肾盂连接处梗阻。所有疝均通过腹部入路修复。随访期间无并发症或复发。总之,对于长期存在呼吸道症状的病例和/或出现无法解释的放射影像(尤其是右心膈区)时,鉴别诊断应考虑莫尔加尼疝。