Meling T R, Tveten S, Due-Tonnessen B J, Skjelbred P, Helseth E
Department of Neurosurgery, National Hospital, Ullevaal Hospital, Oslo, Norway.
Pediatr Neurosurg. 2000 Aug;33(2):89-94. doi: 10.1159/000028982.
We present 2 children with severe syndromal craniosynostosis who were in need of urgent midface advancement surgery due to recurrent ocular dislocations (Pfeiffer's syndrome type II) or severe upper respiratory obstruction (Crouzon's syndrome). They were operated using distraction osteogenesis, with gradual midface or monobloc advancements. In the Pfeiffer patient, a maxillary distraction of 25 mm achieved effective cessation of ocular dislocations, whereas a 23-mm monobloc advancement in the Crouzon patient achieved cessation of nocturnal arterial desaturations. No major postoperative complications were recorded. Distraction osteogenesis has become a versatile and safe technique that allows for large skeletal advancements.
我们报告了2例患有严重综合征性颅缝早闭的儿童，由于反复发生眼球脱位（II型Pfeiffer综合征）或严重上呼吸道梗阻（Crouzon综合征），他们需要紧急进行面中部前移手术。他们接受了牵张成骨手术，面中部或整块骨逐渐前移。在患有Pfeiffer综合征的患者中，上颌骨牵张25毫米有效地停止了眼球脱位，而在患有Crouzon综合征的患者中，整块骨前移23毫米停止了夜间动脉血氧饱和度下降。未记录到重大术后并发症。牵张成骨已成为一种通用且安全的技术，可实现大面积骨骼前移。
