结节性硬化症的肺部受累：一例报告

Pulmonary involvement in tuberous sclerosis complex: presentation of a case.

作者信息

Vitto M, Fabiani F, Capuzi P, D'Angeli A L, Mariotti A B, Bianchi E L, Fiorucci C, Schmid G

机构信息

Department of Cardiovascular and Respiratory Sciences, University La Sapienza, Rome, Italy.

出版信息

Eur Rev Med Pharmacol Sci. 1999 Jul-Aug;3(4):171-3.

PMID:11073123

Abstract

A clinical case of a pulmonary involvement in Tuberous Sclerosis Complex is reported. This rare involvement (1%) is characterized by either interstitial disease or bullae; therefore, pneumothorax is likely to happen in lung parenchyma. Furthermore this complication induces a progressive serious respiratory failure until the death of the patient.

摘要

报告了一例结节性硬化症合并肺部受累的临床病例。这种罕见的受累情况（1%）表现为间质性疾病或肺大疱；因此，气胸很可能在肺实质中发生。此外，这种并发症会导致进行性严重呼吸衰竭，直至患者死亡。