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[髓鞘化视网膜神经纤维。文献综述]

[Myelinated retinal nerve fibers. Review of the literature].

作者信息

Velasque L, Mortemousque B

机构信息

Service d'Ophtalmologie, Hôpital d'Instruction des Armées Robert Picqué, 351 route de Toulouse, 33000 Bordeaux.

出版信息

J Fr Ophtalmol. 2000 Nov;23(9):892-6.

PMID:11084448
Abstract

We describe the clinical findings and diagnostic particularities of myelinated retinal nerve fibers observed in a personal case and review the literature. An 8-year-old child was referred for bilateral papillary abnormalities. The diagnosis was myelinated retinal nerve fibers as white striated patches with feathery edges. Myelinated retinal nerve fibers are a developmental anomaly which may be continuous or discontinuous with the optic nerve head. They are reported to occur in 0.57% to 0.98% of ophthalmic patients. The pathogenesis has not been established. Myelinated retinal nerve fibers are clinically conspicuous. Although they are generally believed to be benign lesions, they occasionally are associated with ocular complications such as myopia.

摘要

我们描述了在一个个人病例中观察到的有髓鞘视网膜神经纤维的临床发现和诊断特点,并对文献进行了综述。一名8岁儿童因双侧乳头异常前来就诊。诊断为有髓鞘视网膜神经纤维,表现为白色条纹状斑块,边缘呈羽毛状。有髓鞘视网膜神经纤维是一种发育异常,可能与视神经乳头连续或不连续。据报道,它们在眼科患者中的发生率为0.57%至0.98%。其发病机制尚未明确。有髓鞘视网膜神经纤维在临床上较为明显。虽然它们通常被认为是良性病变,但偶尔也会与近视等眼部并发症相关。

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