Binaghi S, Gudinchet F, Rilliet B
Department of Radiology, University Hospital of Lausanne, CHUV, 1011 Lausanne, Switzerland.
Pediatr Radiol. 2000 Dec;30(12):856-60. doi: 10.1007/s002470000343.
To assess the value of three-dimensional CT (3D CT) in the diagnosis and management of suspected paediatric craniofacial malformations.
Twenty-eight children (12 girls, 16 boys) with a mean age of 4 years, suffering from craniofacial or cervical malformations, underwent craniofacial spiral CT. 3D reformatting was performed using an independent work-station.
3D CT allowed the preoperative evaluation of 16 patients with craniosynostosis and the post-surgical management of 2 patients. 3D CT clearly depicted malformations of the skull base involving the petrous bone in seven patients (four cases of Goldenhar-Gorlin syndrome, one case of Treacher-Collins syndrome and two cases of Crouzon's disease). Four patients with craniofacial clefts were also evaluated. Radiological findings were confirmed by the clinical and intraoperative findings in all patients that underwent surgical treatment. Movement artefacts and "Lego effect" related to abrupt change of cranial vault border were encountered and are discussed.
3D CT of the skull can safely and reliably identify paediatric craniofacial malformations involving bone, and it should be used as morphological mapping to help the surgeon in planning surgical treatment.
评估三维CT（3D CT）在疑似小儿颅面畸形诊断和治疗中的价值。
28例平均年龄4岁、患有颅面或颈部畸形的儿童接受了颅面螺旋CT检查。使用独立工作站进行三维重建。
3D CT对16例颅缝早闭患者进行了术前评估，并对2例患者进行了术后管理。3D CT清晰显示了7例累及颞骨岩部的颅底畸形（4例Goldenhar-Gorlin综合征、1例Treacher-Collins综合征和2例Crouzon病）。还对4例颅面裂患者进行了评估。所有接受手术治疗的患者，其影像学表现均得到临床和术中发现的证实。遇到了与颅顶边界突然变化相关的运动伪影和“乐高效应”并进行了讨论。
颅骨3D CT能够安全可靠地识别涉及骨骼的小儿颅面畸形，应将其用作形态学图谱，以帮助外科医生规划手术治疗。
