胚胎发育不良性神经上皮肿瘤与小脑萎缩：病例报告

Dysembryoplastic neuroepithelial tumour and cerebellar atrophy: case report.

作者信息

Argyropoulou M I, Arvanitis D L, Tzoufi M, Fanis S L, Papadopoulou Z L, Efremidis S C

机构信息

Department of Radiology, University of Ioannina Medical School, Greece.

出版信息

Neuroradiology. 2001 Jan;43(1):73-5. doi: 10.1007/s002340000476.

DOI:10.1007/s002340000476

PMID:11214654

Abstract

Dysembryoplastic neuroepithelial tumours (DNET) are mainly benign cortical lesions. DNET in the caudate nucleus, thalamus, hypothalamus, pons and cerebellar hemispheres has also been reported. We describe a fronto-temporo-parietal DNET extending to the ipsilateral thalamus and internal capsule, associated with cerebellar lobe atrophy. Involvement of the internal capsule and complication of DNET with cerebellar atrophy have not been reported previously. We emphasise the importance of early diagnosis and treatment of this rare condition.

摘要

胚胎发育不良性神经上皮肿瘤（DNET）主要是良性皮质病变。尾状核、丘脑、下丘脑、脑桥和小脑半球的DNET也有报道。我们描述了一例额颞顶叶DNET延伸至同侧丘脑和内囊，并伴有小脑叶萎缩。内囊受累以及DNET合并小脑萎缩的情况此前未见报道。我们强调了对这种罕见疾病进行早期诊断和治疗的重要性。