Antón-Pacheco Sánchez J, Villafruela Sanz M A, Cuadros García J, Luna Paredes C, Martínez Gimeno A, Berchi García F J
Unidad de la Via Aérea Pediátrica. Servicio de Cirugía Pediátrica, Hospital Materno-Infantil 12 de Octubre. Madrid.
An Esp Pediatr. 2001 Jan;54(1):86-8.
A tracheostomy was performed in a 4-month-old girl with Crouzon's syndrome because of upper respiratory obstruction. During the procedure the absence of tracheal rings was observed. These findings were confirmed by postoperative bronchoscopy. Subsequent surgical correction of the patient's craniofacial anomalies enabled decannulation when the patient was 10 months old. Complete cartilaginous trachea is very rare and is always associated with craniosynostotic syndromes. Tracheobronchial anomalies should be investigated in patients whose respiratory symptoms are not due to upper airway obstruction.
一名4个月大患有克鲁宗综合征的女孩因上呼吸道梗阻接受了气管切开术。手术过程中观察到气管环缺失。这些发现通过术后支气管镜检查得到证实。随后对患者颅面畸形进行的手术矫正使患者在10个月大时能够拔管。完整的软骨气管非常罕见，且总是与颅缝早闭综合征相关。对于呼吸道症状并非由上气道梗阻引起的患者，应调查其气管支气管异常情况。
