Marcão I, Fonseca P, Pereira M S, Ramos A, Fontes L, Amorim H, Marques C, Borges L
Serviço de Medicina-Hospital do Desterro, Lisboa.
Rev Port Cardiol. 2001 Jan;20(1):65-71.
A case of angiosarcoma of the right atrium in a 59-year-old woman is reported, presenting as a recurrent hematic pericardial effusion. The usefulness of echocardiography in making the diagnosis is emphasized. The tumor was already disseminated at the time of the diagnosis. The patient was on palliative therapy, dying a few months later. The histological examination was done at autopsy. This case highlights the difficulty in diagnosis and the various modalities available for an accurate diagnosis of a rare clinical entity. It has a rapid and aggressive course with a very poor prognosis.
报告了一例59岁女性右心房血管肉瘤病例,表现为复发性血性心包积液。强调了超声心动图在诊断中的作用。诊断时肿瘤已发生播散。患者接受姑息治疗,数月后死亡。尸检时进行了组织学检查。该病例突出了诊断的困难以及可用于准确诊断这一罕见临床实体的各种方法。其病程迅速且侵袭性强,预后极差。