Guida F, Rapanà A, Conti C, Cagliari E, Civelli F, Trincia G
Neurosurgical Division, Umberto I Hospital, Venice, Italy.
Childs Nerv Syst. 2001 Apr;17(4-5):297-301. doi: 10.1007/s003810000414.
Aneurysmal bone cysts (ABC) are benign osteolytic lesions that are more common in young people than in adults and involve the skull only exceptionally. The origin of ABC is still debated; indeed, some authors consider ABC to be an anomalous bony reaction that is secondary to traumas or tumours. Conversely, others consider ABC to be a distinct entity. A case of a healthy young female affected by a left frontal ABC is reported here. The clinical onset was characterised by the sudden appearance of a tender and mildly painful frontal mass. Neuroradiological assessment showed a well-circumscribed lytic lesion of the frontal bone with predominantly outward extension. En bloc surgical removal of the lesion was successfully achieved; a reconstructive cranioplasty was also performed to repair the cranial defect. The rarity of the condition described, together with the absence of clear guidelines, prompted us to review the more recent literature with the twin goals of identifying radiological features and becoming able to address the diagnosis and rules for treatment of such a rare entity.
动脉瘤样骨囊肿(ABC)是一种良性溶骨性病变,在年轻人中比成年人更常见,仅极少数累及颅骨。ABC的起源仍存在争议;事实上,一些作者认为ABC是继发于创伤或肿瘤的一种异常骨反应。相反,另一些人则认为ABC是一种独特的实体。本文报道了一例健康年轻女性患左侧额叶ABC的病例。临床起病表现为额部出现一个压痛且轻度疼痛的肿块。神经放射学评估显示额骨有一个边界清晰的溶骨性病变,主要向外扩展。成功地整块手术切除了病变;还进行了颅骨成形术以修复颅骨缺损。所述病症的罕见性以及缺乏明确的指南,促使我们回顾最新文献,以期确定其放射学特征,并能够处理这种罕见实体的诊断和治疗规则。