Wendt S, Flügel W, Spuler A, Mairinger T, Hoch H, Bloching M
Klinik für HNO-Heilkunde, Kopf- und Halschirurgie und Kommunikationsstörungen, HELIOS Klinikum, Schwanebecker Chaussee 50, 13125, Berlin Buch, Deutschland.
HNO. 2010 Jan;58(1):57-62. doi: 10.1007/s00106-009-2035-8.
Aneurysmal bone cyst is a benign osteolytic lesion in childhood and adolescence which primarily arises in metaphyseal long bones. Its presence in bones of the skull base is very rare. In a 3-year old girl presenting with proptosis, MRI demonstrated a well-defined displacing growing mass in the ethmoid sinus, orbita and anterior fossa. The histopathologic examination of biopsy specimens confirmed an aneurysmal bone cyst. Despite radical surgery the child suffered from two recurrences of the lesion in the first year after initial diagnosis. There has been no subsequent recurrence during the last 3 years. Since this lesion is rarely seen at the skull base, is difficult to differentiate clinically and by histopathology and may take an abnormal course, it is described in this case report to emphasize that it should be included in the differential diagnosis of ENT tumors at this location.
动脉瘤样骨囊肿是儿童和青少年时期的一种良性溶骨性病变,主要发生于长骨干骺端。其出现在颅底骨非常罕见。一名3岁女童因眼球突出就诊,MRI显示筛窦、眼眶和前颅窝有一个边界清晰、有占位效应的生长性肿块。活检标本的组织病理学检查证实为动脉瘤样骨囊肿。尽管进行了根治性手术,但患儿在初次诊断后的第一年仍出现了两次病变复发。在过去3年中未再复发。由于该病变在颅底很少见,临床及组织病理学上难以鉴别,且可能呈现异常病程,故本病例报告予以描述,以强调在该部位的耳鼻喉肿瘤鉴别诊断中应考虑到该病。