Cohen Meryl S., Rychik Jack
Division of Cardiology, Department of Pediatrics, The Children's Hospital of Philadelphia, Philadelphia, PA.
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 1999;2:189-202. doi: 10.1016/s1092-9126(99)70016-5.
Left ventricular hypoplasia is associated with a variety of congenital heart defects, including critical aortic stenosis, unbalanced atrioventricular canal, and total anomalous pulmonary venous connection, and is almost uniformly fatal without surgical or catheter-directed intervention. Accurately determining whether the left ventricle can adequately support the systemic circulation can be challenging and may be approached in a variety of ways, depending on the cardiac defect. The decision is more difficult in the present era of pediatric cardiology and cardiothoracic surgery because other options, such as the Norwood procedure and cardiac transplantation, are available to infants with left ventricular hypoplasia with improving survival. This report is a review of the present understanding of left ventricular hypoplasia and gives suggestions about how to stratify these complex patients to single versus two-ventricle repair. Copyright 1999 by W.B. Saunders Company
左心室发育不全与多种先天性心脏缺陷相关，包括严重主动脉瓣狭窄、不平衡型房室通道和完全性肺静脉异位连接，若不进行手术或导管介入治疗，几乎都会致命。准确判断左心室能否充分支持体循环可能具有挑战性，且根据心脏缺陷的不同，可通过多种方式来进行评估。在当今小儿心脏病学和心胸外科时代，这一决策更加困难，因为对于左心室发育不全的婴儿，还有其他治疗选择，如诺伍德手术和心脏移植，且生存率正在提高。本报告回顾了目前对左心室发育不全的认识，并就如何将这些复杂患者分层为单心室修复或双心室修复提出了建议。版权所有1999年，W.B. 桑德斯公司
