Chérif A, Farhati A, Mechmèche R
Service des Explorations Fonctionnelles Cardiaques, Hôpital la Rabta.
Tunis Med. 2001 Apr;79(4):247-50.
Congenital sinus of valsalva aneurysm is a rare cardiac lesion. Once the aneurysm has ruptured, a large left-to-right shunt is created. Prognosis is grave unless operative intervention is undertaken. The authors present 2 cases (2 male) of congenital aneurysm of the right sinus of valsalva ruptured into the right ventricle. The first patient (52 years) have a history of strenuous exertion followed by acute precordial pain and dyspnea. The second patient (25 years) was asymptomatic. The diagnostic was made by 2D and color doppler echocardiography. The defect was closed with a patch with good postoperative course. The authors emphasise the possible rupture of the congenital aneurysm of the sinus of valsalva after 50 years of age. Echocardiography is certainly the best method for diagnosing the condition and for following up these patients. The prognosis after surgical repair has usually been satisfactory.
先天性瓦氏窦瘤是一种罕见的心脏病变。一旦瘤体破裂，就会形成大量的左向右分流。除非进行手术干预，否则预后很差。作者报告了2例（均为男性）先天性右瓦氏窦瘤破裂入右心室的病例。首例患者（52岁）有剧烈运动史，随后出现急性心前区疼痛和呼吸困难。第二例患者（25岁）无症状。通过二维和彩色多普勒超声心动图做出诊断。用补片封闭缺损，术后病程良好。作者强调50岁以后先天性瓦氏窦瘤可能破裂。超声心动图无疑是诊断该病及对这些患者进行随访的最佳方法。手术修复后的预后通常令人满意。
