Antani J A, Srinivas H V, Shivashankar A
Jpn Heart J. 1975 May;16(3):235-42. doi: 10.1536/ihj.16.235.
A total of 14 cases of papillary muscle dysfunction have been observed in Ehlers Danlos syndrome. Five patients had clinically identifiable syndrome of prolapsing mitral leaflets. This form of rare interesting cardiovascular abnormality in Ehlers Danlos syndrome is discussed. The relevant literature is reviewed.
在埃勒斯-当洛综合征中总共观察到14例乳头肌功能障碍。5例患者临床上可识别为二尖瓣叶脱垂综合征。本文讨论了埃勒斯-当洛综合征中这种罕见且有趣的心血管异常形式,并对相关文献进行了综述。