Lyle W G, Jerath R
Section of Plastic Surgery, Medical College of Georgia, Augusta, USA.
Ann Plast Surg. 2001 Oct;47(4):465-7. doi: 10.1097/00000637-200110000-00021.
Linear scleroderma is an unusual disorder characterized by linear streaks of fibrotic skin involvement, which can lead to severe limb deformities and contractures. The authors present a case of severe wrist contracture in a child with linear scleroderma treated by release of the contracture with coverage of the exposed carpus with an abductor digiti minimi flap and skin graft. Reports of successful treatment of extremity deformities are rare. At 1 year this correction appears to have been successful.
线性硬皮病是一种罕见的疾病，其特征为皮肤出现纤维化的线性条纹，可导致严重的肢体畸形和挛缩。作者报告了1例患有线性硬皮病的儿童出现严重腕关节挛缩的病例，通过松解挛缩并采用小指展肌皮瓣和皮肤移植覆盖暴露的腕骨进行治疗。关于成功治疗肢体畸形的报道很少。在1年时，这种矫正似乎已取得成功。
