Bein G, Wolf D
Z Kardiol. 1975 Jun;64(6):547-61.
The diagnosis of double aortic arch was suspected by oesophagography and subsequently proven by angiography in six children. The patients' age ranged from 14 days to 13 years. The diagnostic value of angiography in establishing the existence of two aortic arches is emphasized, which can easily be performed by right heart catheterization. In five patients the aorta descended to the right of the spine; the left arch was hypoplastic and became stenotic or atretic distal to the subclavian artery. In only one case the aorta descended on the left side. In this case both arches had approximately the same size. Four patients were symptomatic immediately after birth and presented with severe inspiratory stridor. The clinical course was so dramatic that surgery was inevitable at the age of four weeks, at 4, 6 and 7 months respectively. The youngest patient died postoperatively. In the other infants the stridor disappeared only months after surgery. One girl had a stridorous respiration occasionally during infancy, later on she complained of dysphagia. She was operated on at the age of 13 years. The double aortic arch was an incidental finding in a girl of 8 years; surgery was not performed.
6例儿童经食管造影怀疑为双主动脉弓，随后经血管造影确诊。患者年龄从14天至13岁不等。强调了血管造影在确定双主动脉弓存在方面的诊断价值，通过右心导管检查即可轻松完成。5例患者的主动脉在脊柱右侧下行；左弓发育不良，在锁骨下动脉远端狭窄或闭锁。仅1例主动脉在左侧下行。在这种情况下，两个弓大小大致相同。4例患者出生后立即出现症状，表现为严重吸气性喘鸣。临床过程非常严重，分别在4周、4个月、6个月和7个月时不可避免地进行了手术。最年幼的患者术后死亡。其他婴儿术后数月喘鸣才消失。1名女孩在婴儿期偶尔有喘鸣呼吸，后来诉说吞咽困难。她13岁时接受了手术。一名8岁女孩的双主动脉弓是偶然发现的，未进行手术。
