Feist D, Obladen M, Beduhn D
Monatsschr Kinderheilkd (1902). 1975 Jan;123(1):1-8.
In seven children the clinical course of extrahepatic portal vein stenosis was studied angiographically. In all children with splenomegaly it was deemed necessary to perform an X-ray barium examination of the oesophagus. Transsplenic portal venography was performed when oesophageal varices were detected to set up the best scheme for emergency treatment. In our patients with hypersplenism there were no specific bone marrow alterations. In contrast to the literature most of our cases had fibrosis of the liver.
对7例肝外门静脉狭窄患儿的临床病程进行了血管造影研究。对于所有脾肿大的患儿,均认为有必要对食管进行X线钡剂检查。当检测到食管静脉曲张时,进行经脾门静脉造影,以制定最佳的急诊治疗方案。在我们的脾功能亢进患者中,没有特异性的骨髓改变。与文献报道不同的是,我们的大多数病例都有肝纤维化。