Cappele O, Sibert L, Descargues J, Delmas V, Grise P
Service d'Urologie, CHU Rouen, Hôpital Charles Nicolle, 1, rue de Germont, 76031 Rouen.
Surg Radiol Anat. 2001;23(4):229-35. doi: 10.1007/s00276-001-0229-1.
The urachus is an embryonic remnant resulting from involution of the allantoic duct and the ventral cloaca. Attaching the bladder dome to the umbilicus, this duct becomes progressively obliterated during fetal life. It may subsequently persist as different variants after birth, some regarded as normal, others as pathologic, due to incomplete closure. Six pediatric cases are reported here, and the literature on the embryology and anatomic basis of the duct is discussed. The urachus is present in nearly 100% of children at birth, with several possible shapes: tubular, fusiform or funnel. It gradually regresses and is found in only a third of adults. Its length varies from 1 to 15 cm. In our series 6 patients showed defective closure of the duct, including 3 with complete patency, 1 cyst, 1 diverticulum and 1 external sinus. Although rare, congenital pathology of the urachus requires a sound knowledge of the anatomy and embryology to distinguish normal forms from those subject to complications. It should be suspected with any lesion in the umbilical region and the appropriate treatment instituted.
脐尿管是尿囊管和泄殖腔腹侧退化后留下的胚胎残余物。该管道将膀胱顶部与脐相连,在胎儿期逐渐闭锁。出生后,由于未完全闭合,它可能会以不同的变体形式持续存在,有些被视为正常,有些则被视为病理状态。本文报告了6例儿科病例,并讨论了有关该管道的胚胎学和解剖学基础的文献。几乎100%的新生儿都有脐尿管,其形状有几种可能:管状、梭形或漏斗形。它会逐渐退化,只有三分之一的成年人中能发现它。其长度从1厘米到15厘米不等。在我们的病例系列中,6例患者显示管道闭合不全,包括3例完全通畅、1例囊肿、1例憩室和1例外部窦道。尽管罕见,但脐尿管的先天性病变需要对解剖学和胚胎学有充分了解,以便区分正常形态和易出现并发症的形态。脐部区域出现任何病变时都应怀疑该病,并采取适当的治疗措施。